PERIOPERATIVE MANAGEMENT IN PATIENT WITH Mc CUNE-ALBRIGHT SYNDROME WITH PATHOLOGICAL PROXIMAL FEMUR FRACTURE

Abstract

The McCune- Albright syndrome is a rare disease diagnosed by the clinical triad of fibrous dysplasia (monostotic or polyostotic), cafe-au lait skin pigmentation, and endocrine hyperfunction. Those patients with bone issues mainly involve long bones and craniofacial anomalies. A 9-year-old male having pathological proximal Left femur fracture with hyperthyroidism, hyperthyroid induced hyperthermia with precocious puberty posted for internal fixation and open deduction for the same fracture. The procedure was done under neuraxial anesthesia without any complications.